Congenital rubella syndrome

This code represents a constellation of birth defects resulting from maternal rubella infection during pregnancy, particularly in the first trimester. The syndrome can affect multiple organ systems, leading to conditions such as congenital heart defects, cataracts, deafness, and developmental delays.

Use this code when documentation clearly indicates a diagnosis of congenital rubella syndrome in an infant or child. This diagnosis is typically made based on a history of maternal rubella infection during pregnancy, characteristic clinical findings, and/or laboratory confirmation of rubella infection in the neonate.

• Always review the medical record for specific manifestations of the syndrome (e.g., congenital heart defects, cataracts) and code them additionally.
• Ensure documentation specifies "congenital" rubella, distinguishing it from acquired rubella.
• Do not confuse with codes for acquired rubella infection (B06.-) in an infant or child.