Congenital Zika virus disease

This code represents a range of birth defects and neurological abnormalities in an infant resulting from maternal Zika virus infection during pregnancy. These manifestations can include microcephaly, intracranial calcifications, ocular abnormalities, and arthrogryposis. It signifies a direct causal link between the mother's Zika infection and the infant's congenital condition.

Use this code when a newborn or infant is diagnosed with congenital anomalies or neurological impairments confirmed to be caused by in-utero exposure to the Zika virus. Documentation should clearly state the diagnosis of congenital Zika syndrome or specific congenital anomalies attributed to maternal Zika infection. This code is appropriate even if the mother was asymptomatic during her pregnancy.

• Ensure documentation explicitly links the infant's condition to congenital Zika virus exposure, not just a general congenital anomaly.
• Do not use this code for infants exposed to Zika in utero but without any diagnosed congenital anomalies.
• Sequence this code as the primary diagnosis when it is the reason for the encounter, followed by codes for specific manifestations (e.g., microcephaly, cerebral calcifications).