Congenital renal failure

This code signifies a condition where the kidneys are congenitally malformed or absent, leading to a complete or near-complete inability to filter waste products from the blood from birth. This is a severe and often life-threatening condition requiring immediate medical intervention.

Use this code for newborns diagnosed with renal agenesis, hypoplasia, or other severe congenital anomalies resulting in end-stage renal disease at birth or shortly thereafter. Documentation should clearly state the congenital nature of the renal failure, often supported by imaging studies and clinical assessment of renal function.

• Distinguish from acquired renal failure in neonates (e.g., due to perinatal asphyxia or sepsis), which would be coded differently.
• Always sequence this code as a principal diagnosis when it is the primary reason for admission or encounter.
• Ensure documentation specifies "congenital" to support the use of this specific P-code.