Macrophthalmos

This code describes an abnormally large eyeball, often present at birth or developing shortly thereafter, that is not associated with elevated intraocular pressure. It can affect one or both eyes and may be accompanied by other ocular anomalies. The condition is distinct from buphthalmos, which is macrophthalmos caused by congenital glaucoma.

Use this code when documentation specifies an enlarged globe without evidence of congenital glaucoma. This typically applies to cases of primary macrophthalmos or megalocornea where the increased eye size is not due to elevated intraocular pressure. Ensure the physician's notes clearly differentiate this from glaucoma-related enlargement.

• Carefully review documentation to rule out congenital glaucoma; if present, code Q15.0.
• Do not use this code for acquired enlargement of the eye due to other conditions.
• Look for associated congenital anomalies that may require additional coding.