Congenital pulmonary valve insufficiency

This code represents a congenital heart defect where the pulmonary valve, present at birth, fails to close properly, leading to a backflow of blood into the right ventricle during diastole. This insufficiency can range from mild to severe, affecting the heart's ability to efficiently pump blood to the lungs.

Use this code for patients diagnosed with pulmonary valve regurgitation that is present from birth. Documentation should clearly state "congenital pulmonary insufficiency" or "congenital pulmonary regurgitation" and may include findings from echocardiograms or cardiac catheterization confirming the diagnosis.

• Differentiate from acquired pulmonary valve insufficiency (I37.1), which develops later in life due to other conditions.
• Code any associated congenital heart defects separately if documented, following sequencing guidelines.
• Ensure the documentation specifies the congenital nature of the insufficiency to support this code.