Congenital tricuspid stenosis

This code represents a congenital heart defect characterized by a narrowing of the tricuspid valve, which regulates blood flow from the right atrium to the right ventricle. This stenosis impedes proper blood flow, leading to increased pressure in the right atrium and reduced output from the right ventricle.

Use this code for documented cases of tricuspid valve stenosis that are present at birth. This diagnosis is typically supported by echocardiography findings, cardiac catheterization reports, and clinical signs of right heart failure or cyanosis in an infant or child.

• Differentiate from acquired tricuspid stenosis (I07.1), which has different etiologies and management.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter.
• Look for documentation specifying "congenital" or "present at birth" to ensure accurate code selection.