Malformation of coronary vessels

This code represents congenital abnormalities in the structure or formation of the coronary arteries or veins. These malformations can include fistulas, aneurysms, or anomalous origins and courses of the coronary vessels, impacting myocardial blood supply.

Apply this code when documentation clearly indicates a congenital anomaly of the coronary vasculature. This typically arises from diagnostic imaging such as echocardiography, CT angiography, or cardiac catheterization, confirming the presence of a structural defect present at birth.

• Differentiate from acquired coronary artery disease (I25.x) which involves atherosclerosis or other non-congenital causes.
• Ensure documentation specifies "congenital" or "malformation" of the coronary vessels; otherwise, consider more general or acquired codes.
• Code any associated cardiac conditions or symptoms separately, such as angina (I20.x) or heart failure (I50.x).