Congenital heart block

This code represents a congenital abnormality of the heart's electrical conduction system, specifically affecting the atrioventricular (AV) node, leading to a slower-than-normal heart rate. It is present at birth and can range in severity from asymptomatic to life-threatening, often requiring pacemaker implantation.

Use this code for patients diagnosed with heart block that is identified as congenital in origin. Documentation should clearly state "congenital heart block" or provide evidence of its presence at birth or early childhood, differentiating it from acquired forms.

• Differentiate from acquired heart block (e.g., I44.x) which has different etiologies and coding.
• Specify the degree of block (first, second, or third) if documented, though this code is for the general congenital form.
• Code any associated congenital heart defects separately if present, as they often co-occur.