Other atresia of aorta

This code represents a congenital malformation where the aorta, the body's main artery, is abnormally narrowed or completely closed at a location other than the aortic valve or the isthmus. This condition obstructs blood flow from the heart to the rest of the body, leading to significant cardiovascular compromise.

Use this code for documented cases of aortic atresia that are not specified as valvular or coarctation. This includes conditions like hypoplastic left heart syndrome where the ascending aorta is severely underdeveloped or atretic. Documentation should clearly indicate the atretic segment of the aorta and specify that it is not the aortic valve or a typical coarctation.

• Differentiate from Q25.21 (Atresia of aortic valve) and Q25.1 (Coarctation of aorta).
• Always sequence as a primary diagnosis when it is the main reason for the encounter.
• Ensure the medical record specifies the exact location of the aortic atresia to support this "other" classification.