Hypoplasia of aorta

This code describes a congenital anomaly characterized by an underdeveloped or abnormally small aorta. This condition can affect any segment of the aorta, leading to reduced blood flow to the body. It is a structural defect present at birth.

Use this code when documentation clearly indicates a diagnosis of hypoplasia of the aorta, often identified during prenatal imaging or in neonates and infants presenting with signs of compromised systemic circulation. Supporting documentation includes echocardiogram reports, cardiac MRI findings, and physician notes detailing the hypoplastic nature of the aorta.

• Differentiate from coarctation of the aorta (Q25.1), which is a localized narrowing, not a generalized underdevelopment.
• Always review imaging reports and operative notes for specific anatomical details and severity.
• Code any associated congenital heart defects or syndromes separately, if documented.