Coarctation of pulmonary artery

This code represents a congenital narrowing of the main pulmonary artery or its branches, restricting blood flow from the right ventricle to the lungs. This coarctation can occur at various points within the pulmonary arterial tree, leading to increased pressure proximal to the narrowing and reduced pressure distally.

Use this code for documented cases of congenital coarctation of the pulmonary artery, identified through echocardiography, cardiac catheterization, or surgical findings. This applies to both isolated coarctation and when it occurs as part of a more complex congenital heart defect.

• Differentiate from pulmonary artery stenosis (Q25.6), which is a broader term encompassing various forms of narrowing, including valvular.
• Always review operative reports and imaging studies for precise anatomical location and severity of the coarctation.
• Code any associated congenital heart defects separately, following sequencing guidelines for multiple congenital anomalies.