Congenital pulmonary arteriovenous malformation

This code describes a birth defect where there are abnormal connections between the pulmonary arteries and veins, bypassing the capillary bed. This malformation can lead to shunting of deoxygenated blood into the systemic circulation, potentially causing hypoxemia and other complications.

Use this code when documentation confirms a congenital arteriovenous malformation specifically located within the pulmonary circulation. This diagnosis is typically made through imaging studies such as CT angiography or echocardiography, often in patients presenting with dyspnea, cyanosis, or hemoptysis.

• Ensure documentation specifies the congenital nature of the malformation to differentiate from acquired forms.
• Look for associated conditions or complications, such as hypoxemia or heart failure, and code them separately if present.
• Do not confuse with other types of congenital malformations of the pulmonary vessels (e.g., Q25.71 for stenosis, Q25.79 for other specified).