Sequestration of lung

This code represents a congenital anomaly where a portion of lung tissue is not connected to the normal tracheobronchial tree and receives its blood supply from the systemic circulation, rather than the pulmonary circulation. This sequestered lung tissue is non-functional and can be intralobar (within a normal lobe) or extralobar (separate from the normal lung).

Use this code for documented cases of pulmonary sequestration identified through imaging studies (e.g., CT scan, MRI) or surgical findings. This diagnosis is typically made in infants or children, but can be discovered incidentally in adults. Documentation should clearly state "sequestration of lung" or specify intralobar/extralobar sequestration.

• Do not confuse with other congenital lung malformations like congenital cystic adenomatoid malformation (CCAM) or bronchogenic cyst.
• Specify laterality (left or right) if documented, using an additional character if available in a more specific code.
• Code any associated symptoms or complications (e.g., infection, hemoptysis) separately.