Congenital cystic lung

This code identifies a congenital malformation of the lung characterized by the presence of abnormal cysts within the pulmonary parenchyma. These cysts are present at birth and result from abnormal embryonic development of the tracheobronchial tree. The condition can manifest as various types of congenital pulmonary airway malformations (CPAMs) or bronchogenic cysts.

Assign this code when documentation clearly indicates a diagnosis of congenital cystic lung, congenital pulmonary airway malformation (CPAM), or congenital bronchogenic cyst. This code is appropriate for newborns, infants, or older individuals diagnosed with this specific birth defect. Supporting documentation includes imaging reports (e.g., prenatal ultrasound, CT scan, MRI) confirming cystic lung lesions present since birth, and pathology reports if surgical resection is performed.

• Do not use this code for acquired cystic lung conditions or cystic fibrosis; these have specific exclusion codes.
• Ensure documentation specifies "congenital" origin to differentiate from other cystic lung diseases.
• Consider additional codes for associated symptoms or complications, such as respiratory distress or infection, if documented.