Congenital cystic lung

This code describes a congenital malformation of the lung characterized by the presence of abnormal cysts or air-filled spaces within the lung tissue. These cysts can vary in size and number, often leading to respiratory distress, recurrent infections, or pneumothorax in infants and children. It encompasses conditions such as congenital cystic adenomatoid malformation (CCAM) and bronchogenic cysts.

Use this code for documented cases of congenital cystic lung disease identified at birth or during early childhood. This diagnosis is typically supported by prenatal ultrasound findings, postnatal chest X-rays, CT scans, or MRI, confirming the presence of cystic lesions within the lung parenchyma. It is appropriate when the primary diagnosis is the congenital malformation itself.

• Differentiate from acquired lung cysts or bullae, which have different etiologies and coding.
• Specify any associated complications, such as infection (e.g., pneumonia) or pneumothorax, with additional codes.
• Review documentation carefully to ensure the congenital nature of the cystic lung disease is clearly stated.