Congenital absence, atresia and stenosis of jejunum

This code describes a birth defect where the jejunum, a part of the small intestine, is either completely missing (agenesis), closed off (atresia), or abnormally narrowed (stenosis). These conditions obstruct the passage of food and fluids, often leading to symptoms like vomiting, abdominal distension, and failure to thrive in neonates.

Use this code for congenital malformations affecting the jejunum that result in absence, complete blockage, or significant narrowing. Documentation should clearly specify the jejunum as the affected segment of the small intestine and confirm the congenital nature of the anomaly, often identified through imaging studies or surgical exploration in newborns.

• Differentiate from acquired strictures or obstructions of the jejunum, which would be coded differently.
• Consider additional codes for associated congenital anomalies or complications, such as malrotation or short bowel syndrome, if documented.
• Ensure the documentation specifies "jejunum" to avoid confusion with other intestinal segments.