Congenital absence, atresia and stenosis of prt sm int

This code signifies a birth defect where a segment of the small intestine, other than the duodenum, jejunum, or ileum specifically, is either completely missing (agenesis), abnormally closed (atresia), or severely narrowed (stenosis). These conditions obstruct the passage of food and digestive fluids, often presenting with symptoms shortly after birth.

Assign this code when documentation specifies a congenital absence, atresia, or stenosis affecting a non-duodenal, non-jejunal, and non-ileal portion of the small intestine. This diagnosis is typically made based on imaging studies (e.g., abdominal X-ray, ultrasound, contrast studies) and confirmed during surgical exploration or autopsy.

• Ensure the documentation clearly specifies "other specified parts of small intestine" to differentiate from codes for duodenum, jejunum, or ileum.
• Do not use this code for acquired strictures or obstructions; it is strictly for congenital anomalies.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, especially for surgical correction.