Ectopic anus

This code represents a congenital anomaly where the anal opening is located in an abnormal position, rather than at the perineum. This malformation can involve the anus opening into the vagina, urethra, or other ectopic sites. It is a type of anorectal malformation (ARM).

Use this code when documentation clearly indicates a diagnosis of an ectopic anus, a congenital condition where the anal opening is misplaced. This diagnosis is typically made at birth or shortly thereafter based on physical examination and imaging studies. Supporting documentation should specify the ectopic location if known.

• Differentiate from imperforate anus without fistula, which involves a complete absence of an anal opening.
• Consider additional codes for associated anorectal malformations or other congenital anomalies if present.
• Ensure documentation specifies "ectopic anus" rather than a general "anorectal malformation" for accurate coding.