Persistent cloaca

This code represents a rare congenital anomaly where the rectum, vagina, and urinary tract all merge into a single common channel, opening to the perineum. It is a complex malformation of the urogenital and anorectal systems.

Assign this code for patients diagnosed with a persistent cloaca, typically identified at birth or shortly thereafter. Documentation should clearly state the presence of a single common channel for the gastrointestinal, urinary, and reproductive systems.

• Ensure documentation specifies "persistent cloaca" rather than other anorectal malformations.
• Code additional congenital anomalies of the genitourinary or digestive systems as appropriate.
• Consider sequencing this code as the primary diagnosis when it is the main reason for admission or encounter.