Congenital rectovaginal fistula

This code describes a birth defect where an abnormal connection exists between the rectum and the vagina. This congenital anomaly allows fecal matter to pass into the vagina, leading to symptoms such as recurrent vaginal infections and passage of gas or stool through the vagina.

Assign this code for neonates, infants, or children diagnosed with a rectovaginal fistula present at birth. Documentation should clearly state the congenital nature of the fistula, distinguishing it from acquired fistulas. This code is appropriate when surgical repair or medical management of this specific congenital defect is being performed.

• Do not code this with Q43.7 (cloaca), as a rectovaginal fistula is a distinct anomaly.
• Ensure documentation specifies "congenital" to differentiate from acquired rectovaginal fistulas, which are coded differently.
• Consider additional codes for associated congenital anomalies or complications, such as imperforate anus, if present.