Congenital single renal cyst

This code describes a birth defect characterized by the presence of a single, fluid-filled sac within one kidney. This condition is present at birth and is not acquired later in life. It typically refers to a non-obstructive, simple cyst.

Use this code when documentation clearly indicates a congenital, solitary renal cyst identified in a patient. This diagnosis is often made via prenatal ultrasound or imaging studies performed in infancy or childhood. The medical record should specify "congenital" and "single" to support its use.

• Differentiate from acquired renal cysts (N28.1) or multiple/polycystic kidney disease (Q61.2, Q61.3, Q61.4).
• Ensure the documentation specifies "single" to avoid confusion with other congenital cystic kidney disorders.
• If the laterality (left or right kidney) is documented, it is not separately coded for this specific diagnosis.