Polycystic kidney, adult type

This code represents autosomal dominant polycystic kidney disease (ADPKD), a genetic disorder characterized by the development of numerous cysts in the kidneys, leading to progressive renal enlargement and eventual kidney failure. It is the most common inherited kidney disease, typically manifesting in adulthood.

Use this code when documentation explicitly states a diagnosis of adult polycystic kidney disease or ADPKD. This diagnosis is often supported by imaging studies (e.g., ultrasound, CT, MRI) showing multiple bilateral renal cysts, family history, and clinical signs of renal impairment.

• Differentiate from other forms of polycystic kidney disease, such as autosomal recessive (infantile type).
• Code any associated complications, such as chronic kidney disease (CKD) stages, hypertension, or urinary tract infections, as secondary diagnoses.
• Ensure documentation specifies "adult type" or "ADPKD" to support the use of this specific code.