Asplenia (congenital)

This code signifies the congenital absence of the spleen, a vital organ involved in immune function and blood filtration. Individuals with this condition are born without a spleen, making them highly susceptible to severe infections.

Assign this code when documentation explicitly states congenital asplenia or absence of the spleen at birth. This is typically identified through imaging studies (e.g., ultrasound, CT scan) or during surgical exploration.

• Differentiate from acquired asplenia (e.g., post-splenectomy), which is coded differently.
• Look for terms like "agenesis of spleen" or "congenital absence of spleen."
• Consider sequencing this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when managing related complications.