Conjoined twins

This code represents a rare congenital anomaly where two fetuses are physically joined together, sharing organs or body structures to varying degrees. The specific type of conjoined twinning (e.g., thoracopagus, omphalopagus) is not differentiated by this code.

Use this code when documentation confirms the diagnosis of conjoined twins, typically identified during prenatal imaging or at birth. This code is appropriate for the maternal record when the mother is carrying conjoined twins, and for the infant's record if born alive.

• This code is for the presence of conjoined twins; additional codes may be needed for specific shared organs or associated anomalies.
• Do not confuse this with multiple gestations (e.g., twins, triplets) that are not conjoined.
• Sequence this code as a principal diagnosis when it is the primary reason for the encounter or hospitalization.