Disorders of bilirubin excretion

This code signifies conditions where the body has difficulty eliminating bilirubin, a byproduct of red blood cell breakdown. This can lead to an accumulation of bilirubin in the blood, often manifesting as jaundice. It encompasses various genetic or acquired defects in the hepatic uptake, conjugation, or excretion of bilirubin.

Use this code for diagnoses such as Dubin-Johnson syndrome, Rotor syndrome, or other specified disorders of bilirubin transport or metabolism that result in impaired excretion. Documentation should clearly indicate a defect in the excretory pathway of bilirubin, rather than overproduction or impaired conjugation.

• Differentiate from hyperbilirubinemia due to hemolysis (e.g., hemolytic anemia) or neonatal jaundice, which have distinct codes.
• Ensure physician documentation specifies the excretion disorder; "jaundice" alone is insufficient.
• Consider additional codes for underlying causes or associated conditions, such as liver disease, if documented.