Tetralogy of fallot

This code represents a complex congenital heart defect characterized by four distinct abnormalities: a ventricular septal defect, pulmonary stenosis, an overriding aorta, and right ventricular hypertrophy. These defects lead to deoxygenated blood bypassing the lungs and entering systemic circulation, causing cyanosis.

Use this code for patients diagnosed with Tetralogy of Fallot, typically identified in infancy or early childhood. Documentation should clearly state the presence of this specific combination of cardiac anomalies, often confirmed by echocardiography or cardiac catheterization.

• Ensure documentation specifies all four components of Tetralogy of Fallot for accurate coding.
• Do not confuse with other cyanotic congenital heart diseases; this code is specific to the four classic defects.
• Code any associated symptoms or complications, such as cyanotic spells or heart failure, as secondary diagnoses.