Tetralogy of Fallot

This code represents Tetralogy of Fallot, a complex congenital heart defect characterized by four distinct abnormalities: a ventricular septal defect (VSD), pulmonary stenosis, an overriding aorta, and right ventricular hypertrophy. This combination leads to deoxygenated blood bypassing the lungs and entering systemic circulation, causing cyanosis.

Use this code when documentation explicitly states a diagnosis of Tetralogy of Fallot. This diagnosis is typically made in infancy or early childhood based on clinical presentation, echocardiography, and cardiac catheterization findings. It is appropriate for both initial diagnosis and ongoing management of this specific congenital heart anomaly.

• Always ensure the documentation clearly specifies "Tetralogy of Fallot" and not a general congenital heart defect.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter.
• Do not confuse with other cyanotic congenital heart defects; ensure the four characteristic components of Tetralogy of Fallot are either stated or implied by the diagnosis.