Congenital musculoskeletal deformities of skull, face, and jaw

This code represents various congenital structural abnormalities affecting the bones of the skull, facial skeleton, and mandible. These deformities are present at birth and can range from minor cosmetic issues to significant functional impairments impacting breathing, feeding, and speech. Examples include craniosynostosis, facial clefts (excluding cleft lip/palate), and mandibular hypoplasia.

Use this code when documentation clearly identifies a congenital malformation of the skull, face, or jaw bones. This applies to conditions diagnosed at birth or later in life, provided the etiology is congenital. Supporting documentation includes physician notes detailing the specific deformity, imaging reports (e.g., X-rays, CT scans), and genetic testing results if applicable.

• Do not use this code for cleft lip or cleft palate; refer to codes in the 749 series.
• Ensure the documentation specifies a congenital origin; acquired deformities are coded elsewhere.
• Code any associated functional impairments or syndromes separately, if applicable.