Localized scleroderma [morphea]

This code identifies a chronic autoimmune connective tissue disorder characterized by localized patches of hardened, thickened skin. Morphea typically presents as waxy, ivory-colored plaques that can vary in size and depth, affecting the dermis and sometimes the subcutaneous tissue, but generally sparing internal organs.

Apply this code when documentation specifies localized scleroderma, such as plaque morphea, generalized morphea, linear morphea, or deep morphea. The physician's notes should clearly indicate the diagnosis of morphea based on clinical examination and/or biopsy findings.

• Do not use this code for systemic sclerosis (scleroderma), which involves internal organ involvement.
• Specify the type of morphea if documented (e.g., linear, generalized) using additional codes if available and appropriate.
• Ensure documentation differentiates localized morphea from other skin conditions like lichen sclerosus or atrophoderma of Pasini and Pierini.