Linear scleroderma

This code represents a localized form of scleroderma characterized by a linear band of thickened, hardened skin and subcutaneous tissue. It often appears as a "coup de sabre" lesion on the head or a linear streak on an extremity, potentially affecting underlying muscle and bone.

Use this code for patients diagnosed with linear scleroderma, a subtype of localized scleroderma. Documentation should clearly describe the linear presentation of skin induration and atrophy, often noting its distribution (e.g., limb, forehead). This diagnosis is typically made clinically, sometimes supported by biopsy.

• Differentiate from generalized scleroderma (systemic sclerosis), which involves widespread skin hardening and internal organ involvement.
• Do not confuse with morphea (L94.0), which presents as circumscribed plaques rather than linear bands.
• Code any associated complications, such as joint contractures or limb length discrepancy, separately.