Circumscribed scleroderma

This code represents a chronic autoimmune connective tissue disorder characterized by localized hardening and thickening of the skin and sometimes underlying tissues. It is also known as morphea, and it does not typically involve internal organs. The condition can manifest as single or multiple patches, linear streaks, or generalized forms.

Use this code when documentation specifies a diagnosis of circumscribed scleroderma or morphea. This applies to patients presenting with localized skin induration and discoloration without systemic involvement. Supporting documentation should clearly distinguish it from systemic sclerosis.

• Differentiate carefully from systemic sclerosis (generalized scleroderma), which involves internal organs and has different code assignments.
• Ensure the physician's documentation explicitly states "circumscribed" or "morphea" to support this specific code.
• Do not use for other localized skin conditions that may present with hardening, such as lichen sclerosus et atrophicus, without a definitive diagnosis of scleroderma.