Other von Willebrand disease

This code signifies a diagnosis of von Willebrand disease (vWD) that does not fall into a specified type (e.g., Type 1, Type 2A, 2B, 2M, 2N, or Type 3). It represents a qualitative or quantitative defect in von Willebrand factor (vWF) leading to impaired platelet adhesion and aggregation, resulting in a bleeding diathesis.

Use this code when the medical record clearly documents von Willebrand disease but does not specify a particular type, or when the specific type identified does not have a more granular ICD-10-CM code. This is appropriate for cases where diagnostic testing confirms vWD but further subtyping is pending or inconclusive, or for less common variants not otherwise classified.

• Ensure documentation explicitly states "von Willebrand disease, unspecified type" or "other von Willebrand disease."
• Avoid using this code if a specific type of von Willebrand disease (e.g., Type 1, Type 2A, Type 3) is documented; use the more specific code instead.
• Code any associated bleeding manifestations or complications separately, if applicable.