Double outlet right ventricle

This code represents a congenital heart defect where both the aorta and the pulmonary artery originate entirely or predominantly from the right ventricle. This malformation results in a mixing of oxygenated and deoxygenated blood, leading to varying degrees of cyanosis and heart failure depending on associated defects.

Use this code when documentation explicitly states "double outlet right ventricle" as a congenital anomaly. This diagnosis is typically made prenatally or in infancy based on echocardiography and confirmed with cardiac catheterization or MRI.

• Always code any associated cardiac anomalies (e.g., ventricular septal defect, pulmonary stenosis) in addition to this code.
• Specify the type of double outlet right ventricle (e.g., subaortic, subpulmonary, doubly committed, non-committed) if documented, as this impacts clinical management.
• Do not confuse with other complex congenital heart diseases like Tetralogy of Fallot or truncus arteriosus; these are distinct conditions.