Discordant ventriculoarterial connection

This code describes a congenital heart defect where the great arteries (aorta and pulmonary artery) are connected to the ventricles in an abnormal fashion. Specifically, the aorta originates from the right ventricle and the pulmonary artery originates from the left ventricle, leading to two parallel circulations. This condition is also known as complete transposition of the great arteries (TGA).

Use this code for patients diagnosed with complete transposition of the great arteries. Documentation should clearly indicate the abnormal connection of the aorta to the right ventricle and the pulmonary artery to the left ventricle. This code is applicable for initial diagnosis and subsequent encounters related to this specific congenital anomaly.

• Do not confuse with congenitally corrected TGA (L-TGA), which has a different code.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter.
• Look for documentation of associated defects, such as VSD or ASD, and code them separately.