Discordant atrioventricular connection

This code represents a congenital heart defect where the atria are connected to the ventricles in an abnormal fashion. Specifically, the right atrium connects to the morphological left ventricle, and the left atrium connects to the morphological right ventricle, often referred to as congenitally corrected transposition of the great arteries (CCTGA) or L-transposition. This results in the systemic circulation being supplied by the morphological right ventricle and the pulmonary circulation by the morphological left ventricle.

Use this code when documentation clearly indicates a diagnosis of discordant atrioventricular connection, such as congenitally corrected transposition of the great arteries (CCTGA). This diagnosis is typically established through echocardiography, cardiac MRI, or cardiac catheterization. The physician's diagnostic statement must explicitly state this specific anatomical anomaly.

• Do not confuse this with D-transposition of the great arteries (TGA), which involves discordant ventriculoarterial connections.
• Always look for documentation specifying the type of transposition (e.g., "congenitally corrected" or "L-transposition") to ensure accurate coding.
• Code any associated cardiac anomalies, such as ventricular septal defects or pulmonary stenosis, with additional codes.