Double outlet left ventricle

This code describes a congenital heart defect where both the aorta and the pulmonary artery originate entirely or predominantly from the left ventricle. This malformation results in abnormal blood flow patterns, often leading to cyanosis and heart failure if uncorrected. It is a complex anomaly requiring surgical intervention.

Use this code when documentation clearly indicates that both great arteries arise from the left ventricle. This diagnosis is typically made through echocardiography, cardiac MRI, or cardiac catheterization. It applies to patients diagnosed with this specific anatomical arrangement of the great vessels.

• Differentiate from double outlet right ventricle (DORV), which is a distinct anomaly.
• Always code associated cardiac anomalies, such as ventricular septal defects (VSDs) or pulmonary stenosis, if present.
• Ensure the documentation specifies "left ventricle" as the origin for both great arteries to support this code.